Fact 9: Huntington’s Disease in Children – The Rarity of Juvenile Onset
While HD typically manifests in adulthood, there are rare instances where it occurs in children and teenagers. This is referred to as juvenile Huntington’s Disease (JHD), accounting for a small fraction of all HD cases.
JHD often presents differently from adult-onset HD. Instead of chorea, children might exhibit rigidity, slow movements, and tremors. There could also be a rapid decline in school performance and significant behavioral changes. These could be the first indications of JHD, often preceding motor symptoms.
The progression of JHD is usually more rapid than the adult-onset form, highlighting the devastating impact it can have on affected families. Coping with such an aggressive disease in a child can be emotionally overwhelming and requires extensive support, both medically and socially.
However, ongoing research and advancements in treatment are shedding light on JHD. There’s hope that with time, we will be better equipped to manage this aggressive form of HD and perhaps even prevent its onset in those at risk. (9)
